spinocerebellar ataxia type 40

ORPHA: 423275

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spinocerebellar ataxia type 40, sourced from HPO and Orphanet clinical annotations.

Vertical supranuclear gaze palsyDysarthriaDysmetriaHyperreflexiaGait ataxiaDysdiadochokinesisIntention tremorBroad-based gaitAbnormal speech patternScanning speechSpastic paraparesisUnsteady gaitFunctional motor deficitPontocerebellar atrophy

Classification & Codes

Orphanet Code

ORPHA:423275
spinocerebellar ataxia type 40
OrphanetORPHA:423275
Treatments0 drug(s)
Symptoms on record14 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO