spinocerebellar ataxia type 5

ORPHA: 98766

Overview

autosomal dominant cerebellar ataxia that is characterized by the early-onset of cerebellar signs and eye movement abnormalities with a very slow disease progression, and has material basis in mutation in the SPTBN2 gene

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spinocerebellar ataxia type 5, sourced from HPO and Orphanet clinical annotations.

Cerebellar atrophyGait disturbanceSlurred speechIncoordination

Classification & Codes

Orphanet Code

ORPHA:98766
spinocerebellar ataxia type 5
OrphanetORPHA:98766
Treatments0 drug(s)
Symptoms on record4 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO