spondylocarpotarsal synostosis syndrome

MeSH: C535780ORPHA: 3275

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spondylocarpotarsal synostosis syndrome, sourced from HPO and Orphanet clinical annotations.

Hearing impairmentPectus carinatumTalipes equinovarusScoliosisLumbar hyperlordosisIntervertebral space narrowingVertebral fusionDisproportionate short statureEnamel hypoplasiaTarsal synostosisCarpal synostosisCleft palateShort neckDelayed ossification of carpal bonesPes planusFrontal bossingDelayed skeletal maturation

Classification & Codes

MeSH Code

C535780

Orphanet Code

ORPHA:3275
spondylocarpotarsal synostosis syndrome
MeSHC535780
OrphanetORPHA:3275
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO