spondyloepimetaphyseal dysplasia, Irapa type

MeSH: C562958ORPHA: 93351

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spondyloepimetaphyseal dysplasia, Irapa type, sourced from HPO and Orphanet clinical annotations.

Pectus carinatumAbnormal rib morphologyPlatyspondylyOsteoporosisAbnormal metaphysis morphologyBroad palmAbnormal carpal morphologyGait disturbanceAbnormal joint morphologyLimitation of joint mobilityPes planusBroad footSpondyloepimetaphyseal dysplasiaOsteoarthritisCoxa varaArthralgiaGenu valgumMicromeliaShort palmSynostosis of carpal bonesAbnormal epiphysis morphologyHypoplastic pelvisDisproportionate short-limb short statureUpper limb undergrowthShort metacarpalShort metatarsal

Classification & Codes

MeSH Code

C562958

Orphanet Code

ORPHA:93351
spondyloepimetaphyseal dysplasia, Irapa type
MeSHC562958
OrphanetORPHA:93351
Treatments0 drug(s)
Symptoms on record26 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO