spondyloepimetaphyseal dysplasia, Shohat type

MeSH: C566523ORPHA: 93352

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spondyloepimetaphyseal dysplasia, Shohat type, sourced from HPO and Orphanet clinical annotations.

PlatyspondylyScoliosisArthralgiaFlared metaphysisMetaphyseal wideningShort long bonePremature osteoarthritisAbnormal vertebral morphologyDisproportionate short statureSevere short statureThoracic hypoplasiaAbnormal epiphysis morphologyGeneralized bone demineralizationCentral vertebral hypoplasiaShort neckHepatosplenomegalyLaryngeal stenosisHoarse voiceDelayed epiphyseal ossificationTracheal stenosisUpper airway obstructionVertebral compression fractureGenu varumBowing of the legsMetaphyseal irregularityFibular overgrowthAbdominal distentionHyperlordosisSquared-off platyspondylyNarrow vertebral interpedicular distanceLimb undergrowthAbnormal bronchus morphologyJoint hypermobility

Classification & Codes

MeSH Code

C566523

Orphanet Code

ORPHA:93352
spondyloepimetaphyseal dysplasia, Shohat type
MeSHC566523
OrphanetORPHA:93352
Treatments0 drug(s)
Symptoms on record33 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO