sporadic idiopathic steroid-resistant nephrotic syndrome

ORPHA: 84271

Overview

Steroid-resistant, sporadic idiopathic nephrotic syndrome, is a heterogeneous entity. Nephrotic syndrome is characterised by marked proteinuria, with reduced plasmatic levels of albumin, and potentially with oedema.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

Orphanet Code

ORPHA:84271
sporadic idiopathic steroid-resistant nephrotic syndrome
OrphanetORPHA:84271
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
sporadic idiopathic steroid-resistant nephrotic syndrome | OrphanDrug