STAR syndrome

MeSH: C567475ORPHA: 140952

Overview

This syndrome is characterised by the association of toe syndactyly, facial dysmorphism including telecanthus (abnormal distance between the eyes) and a broad nasal tip, urogenital malformations and anal atresia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with STAR syndrome, sourced from HPO and Orphanet clinical annotations.

Lop earToe syndactylyAnal atresiaClinodactyly of the 5th fingerShort statureLabial hypoplasiaVesicoureteral refluxRenal insufficiencyHorseshoe kidneyEctopic kidneyRenal agenesisThin upper lip vermilionBulbous noseWide nasal bridgeTelecanthusBicornuate uterusAbnormal cardiac septum morphologyClitoral hypertrophyMyopiaRetinal dystrophyEyelid colobomaSeizureAortic regurgitationHypoplasia of the radiusSyringomyeliaPulmonary artery stenosisMacular dystrophyMitral atresia

Classification & Codes

MeSH Code

C567475

Orphanet Code

ORPHA:140952
STAR syndrome
MeSHC567475
OrphanetORPHA:140952
Treatments0 drug(s)
Symptoms on record28 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
STAR syndrome | OrphanDrug