Steinfeld syndrome

MeSH: C566655ORPHA: 3186

Overview

Holoprosencephaly-radial heart renal anomalies syndrome is characterised by holoprosencephaly, predominantly radial limb deficiency (absent thumbs, phocomelia), heart defects, kidney malformations and absence of gallbladder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Steinfeld syndrome, sourced from HPO and Orphanet clinical annotations.

MicrocephalyAbnormality of the outer earAtresia of the external auditory canalHoloprosencephalyAplasia of the noseOrofacial cleftMicrophthalmiaHypoplasia of the radiusHypoplasia of the ulnaVertebral segmentation defectAplasia/Hypoplasia of the thumbAbsent gallbladderMedian cleft upper lipHearing impairmentHypotelorismIris colobomaMissing ribsOmphaloceleTetralogy of FallotFoot polydactylyAbnormality of neuronal migrationOverriding aortaRenal hypoplasia/aplasiaPhocomeliaCyclopiaAbnormal localization of kidneyAbnormal humerus morphology

Classification & Codes

MeSH Code

C566655

Orphanet Code

ORPHA:3186
Steinfeld syndrome
MeSHC566655
OrphanetORPHA:3186
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Steinfeld syndrome | OrphanDrug