stiff-person syndrome

MeSH: D016750ORPHA: 3198

Overview

rare neurologic disorder characterized by progressive rigidity and stiffness in truncal muscles, spasms, postural deformities, chronic pain, impaired mobility, and lumbar hyperlordosis

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with stiff-person syndrome, sourced from HPO and Orphanet clinical annotations.

AnxietyHyperhidrosisFallsEMG abnormalityIntermittent painful muscle spasmsEmotional labilityAgoraphobiaGait disturbanceMyoclonusHyperreflexiaDysphagiaConstipationRigidityExaggerated startle responseMyalgiaParaspinal muscle hypertrophyAutoimmune antibody positivityCognitive impairmentAnti-Amphiphysin antibodyAnti-DPPX antibodyAnti-GAD65 antibodyAnti-Gephyrin antibodyAnti-GlyR antibodyDiplopiaDiabetes mellitusHypothyroidismApneaVertigoLumbar hyperlordosisFreezing of gait

Classification & Codes

MeSH Code

D016750

Orphanet Code

ORPHA:3198
stiff-person syndrome
MeSHD016750
OrphanetORPHA:3198
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
stiff-person syndrome | OrphanDrug