subacute sclerosing panencephalitis
ICD-10: A81.1MeSH: D013344ORPHA: 2806
Overview
rare insidious sequela from measles infection
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with subacute sclerosing panencephalitis, sourced from HPO and Orphanet clinical annotations.
Atypical behaviorMental deteriorationMyoclonusDepressionDementiaIrritabilityHallucinationsDelusionSeizureLethargyGait disturbanceDystoniaSleep disturbanceLoss of speechEEG with periodic complexesAbnormal autonomic nervous system physiologyChorioretinitisBrain atrophyAkinetic mutismPeriventricular white matter hyperintensitiesVegetative stateMotor regressionAnti-measles antibody positivityVisual lossRetinal hemorrhagePapilledemaAtaxiaSpasticityAbnormality of extrapyramidal motor functionVentriculomegalyCSF pleocytosisReduced brain N-acetyl aspartate level by MRSAbnormal brain choline/creatine ratio by MRSDyskinesiaCSF oligoclonal immunoglobulin G bands
Classification & Codes
ICD-10 Code
A81.1MeSH Code
D013344Orphanet Code
ORPHA:2806subacute sclerosing panencephalitis
| ICD-10 | A81.1 |
| MeSH | D013344 |
| Orphanet | ORPHA:2806 |
| Treatments | 0 drug(s) |
| Symptoms on record | 35 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO