sucrose intolerance
ICD-10: E74.3MeSH: C538139ORPHA: 35710
Overview
Congenital sucrase-isomaltase deficiency (CSID) is a carbohydrate intolerance disorder characterised by malabsorption of oligosaccharides and disaccharides
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with sucrose intolerance, sourced from HPO and Orphanet clinical annotations.
Failure to thriveWeight lossDehydrationDiarrheaOsmotic diarrheaHypernatremiaAbdominal distentionMalnutritionRenal insufficiencyNephrolithiasisVomitingHypercalcemiaHyperactive bowel soundsHematuriaFever
Classification & Codes
ICD-10 Code
E74.3MeSH Code
C538139Orphanet Code
ORPHA:35710sucrose intolerance
| ICD-10 | E74.3 |
| MeSH | C538139 |
| Orphanet | ORPHA:35710 |
| Treatments | 0 drug(s) |
| Symptoms on record | 15 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO