syndromic X-linked intellectual disability 34

ORPHA: 466791

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with syndromic X-linked intellectual disability 34, sourced from HPO and Orphanet clinical annotations.

Relative macrocephalyOpen mouthMalar flatteningLong faceProminent nasal bridgeNarrow nasal bridgeProminent noseStrabismusMyopiaUpslanted palpebral fissureDental crowdingAnxietyDelayed speech and language developmentMild intellectual disabilityGeneralized hypotoniaSlender buildHypernasal speechAbnormal left ventricle morphologyPes planusAbnormal facial shapePoor suckDelayed gross motor developmentPoor head controlHigh, narrow palateKyphoscoliosisDysplastic corpus callosumSynostosis involving the 1st metacarpalFeeding difficultiesExcessive shynessCryptorchidismWide mouthThin upper lip vermilionEpicanthusHypertelorismShort philtrumTriangular faceDownslanted palpebral fissuresWidely spaced teethAutismAggressive behaviorDelayed pubertySeizureAtaxiaCerebellar hypoplasiaPlagiocephalyJoint hypermobilityFailure to thriveVentricular septal defectAtrial septal defectPatent ductus arteriosusPatent foramen ovaleRight ventricular hypertrophyLeft ventricular hypertrophyHallux valgusFrontal bossingGastroesophageal refluxHypoplasia of the corpus callosumIntention tremorPoor speechSupernumerary nippleThickened calvariaObstructive sleep apneaClinodactyly of the 5th fingerTalipes valgusTricuspid regurgitationPseudobulbar paralysisHyperactive patellar reflexChiari type I malformationConfetti-like hypopigmented maculesBilateral cryptorchidismEbstein anomaly of the tricuspid valveAnterior pituitary hypoplasiaSpeech apraxiaThick vermilion borderAbnormal cardiac ventricular functionInfantile constant exotropiaNasogastric tube feeding

Classification & Codes

Orphanet Code

ORPHA:466791
syndromic X-linked intellectual disability 34
OrphanetORPHA:466791
Treatments0 drug(s)
Symptoms on record77 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO