systemic-onset juvenile idiopathic arthritis

ICD-10: M08.2ORPHA: 85414

Overview

Systemic inflammatory disorder, and a subtype of juvenile idiopathic arthritis, associated with fever, rash, and arthritis.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with systemic-onset juvenile idiopathic arthritis, sourced from HPO and Orphanet clinical annotations.

Skin rashArthritisJoint swellingFeverArthralgiaAutoimmunityElevated erythrocyte sedimentation rateJuvenile rheumatoid arthritisElevated circulating C-reactive protein concentrationLymphadenopathyGlomerulonephritisOsteopeniaGrowth delayPericarditisSplenomegalyAbdominal painPleural effusionHepatomegalyIncreased circulating ferritin concentrationElevated pulmonary artery pressureAnterior uveitisNon-infectious meningitis

Classification & Codes

ICD-10 Code

M08.2

Orphanet Code

ORPHA:85414
systemic-onset juvenile idiopathic arthritis
ICD-10M08.2
OrphanetORPHA:85414
Treatments0 drug(s)
Symptoms on record22 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO