systemic-onset juvenile idiopathic arthritis
ICD-10: M08.2ORPHA: 85414
Overview
Systemic inflammatory disorder, and a subtype of juvenile idiopathic arthritis, associated with fever, rash, and arthritis.
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with systemic-onset juvenile idiopathic arthritis, sourced from HPO and Orphanet clinical annotations.
Skin rashArthritisJoint swellingFeverArthralgiaAutoimmunityElevated erythrocyte sedimentation rateJuvenile rheumatoid arthritisElevated circulating C-reactive protein concentrationLymphadenopathyGlomerulonephritisOsteopeniaGrowth delayPericarditisSplenomegalyAbdominal painPleural effusionHepatomegalyIncreased circulating ferritin concentrationElevated pulmonary artery pressureAnterior uveitisNon-infectious meningitis
Classification & Codes
ICD-10 Code
M08.2Orphanet Code
ORPHA:85414systemic-onset juvenile idiopathic arthritis
| ICD-10 | M08.2 |
| Orphanet | ORPHA:85414 |
| Treatments | 0 drug(s) |
| Symptoms on record | 22 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO