Tenosynovial Giant Cell Tumor

ICD-10: 2E80.YORPHA: ORPHA:1000751 Treatment Available

Overview

A rare, locally aggressive neoplasm of the synovium of joints, bursae, and tendon sheaths driven by CSF1 overexpression. Presents as localized or diffuse (pigmented villonodular synovitis) forms.

Available Treatments (1)

DrugFormStatusCountriesLead Time
vimseltinib
Orphan
FDA Approved (2025)1

Classification & Codes

ICD-10 Code

2E80.Y

Orphanet Code

ORPHA:ORPHA:100075
Tenosynovial Giant Cell Tumor
ICD-102E80.Y
OrphanetORPHA:ORPHA:100075
Treatments1 drug(s)
Statuspublished

Treatment Summary

Factual Authority
Last Updated7/24/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO