thanatophoric dysplasia type 2

MeSH: C536508ORPHA: 93274

Overview

form of thanatophoric dysplasia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with thanatophoric dysplasia type 2, sourced from HPO and Orphanet clinical annotations.

Abnormality of the kidneyHydrocephalusMacrocephalyHearing impairmentProptosisNarrow chestPlatyspondylyAbnormal metaphysis morphologyAcanthosis nigricansBrachydactylySeizureHypotoniaHoloprosencephalyLimitation of joint mobilityPolyhydramniosRedundant skinAtrial septal defectPatent ductus arteriosusFrontal bossingEncephaloceleRespiratory insufficiencyVentriculomegalyAbnormality of neuronal migrationSkeletal dysplasiaCloverleaf skullKyphosisMicromeliaShort statureDepressed nasal bridgeAplasia/Hypoplasia of the lungsShort thoraxIncreased nuchal translucencyFlat faceCognitive impairmentJoint hypermobility

Classification & Codes

MeSH Code

C536508

Orphanet Code

ORPHA:93274
thanatophoric dysplasia type 2
MeSHC536508
OrphanetORPHA:93274
Treatments0 drug(s)
Symptoms on record35 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO