Thiemann disease, familial form

MeSH: C537144ORPHA: 3314

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Thiemann disease, familial form, sourced from HPO and Orphanet clinical annotations.

Abnormal metaphysis morphologyBrachydactylyLimitation of joint mobilityAbnormal epiphysis morphologyAvascular necrosis

Classification & Codes

MeSH Code

C537144

Orphanet Code

ORPHA:3314
Thiemann disease, familial form
MeSHC537144
OrphanetORPHA:3314
Treatments0 drug(s)
Symptoms on record5 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO