trichodysplasia-amelogenesis imperfecta syndrome

ORPHA: 79129

Overview

The association of amelogenesis imperfecta and a microscopically typical hair dysplasia has been found in several members of a family in two generations. Transmission is X-linked.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with trichodysplasia-amelogenesis imperfecta syndrome, sourced from HPO and Orphanet clinical annotations.

Amelogenesis imperfectaAlopecia of scalpTrichodysplasia

Classification & Codes

Orphanet Code

ORPHA:79129
trichodysplasia-amelogenesis imperfecta syndrome
OrphanetORPHA:79129
Treatments0 drug(s)
Symptoms on record3 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
trichodysplasia-amelogenesis imperfecta syndrome | OrphanDrug