trimethylaminuria

ICD-10: E88.8MeSH: C536561ORPHA: 2398

Overview

rare metabolic disorder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with trimethylaminuria, sourced from HPO and Orphanet clinical annotations.

Insulin resistanceMultiple lipomasGait disturbanceReduced tendon reflexesJoint stiffnessHepatomegalyArthralgiaParesthesiaAbnormal adipose tissue morphologyPeripheral neuropathyFetor

Classification & Codes

ICD-10 Code

E88.8

MeSH Code

C536561

Orphanet Code

ORPHA:2398
trimethylaminuria
ICD-10E88.8
MeSHC536561
OrphanetORPHA:2398
Treatments0 drug(s)
Symptoms on record11 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO