Tubulointerstitial nephritis and uveitis

MeSH: C536922ORPHA: 91500

Overview

Kidney related medical condition.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Tubulointerstitial nephritis and uveitis, sourced from HPO and Orphanet clinical annotations.

Tubulointerstitial nephritisNongranulomatous uveitisBeta 2-microglobulinuriaRenal lymphocytic tubulitisRenal neutrophilic tubulitisRenal interstitial edemaPapilledemaWeight lossFeverMicroscopic hematuriaElevated circulating creatinine concentrationAnterior uveitisPosterior uveitisDecreased glomerular filtration rateFatigueMild proteinuriaRed eyeSterile pyuriaOcular painVisual impairmentCataractPhotophobiaSkin rashNormochromic anemiaNormocytic anemiaRenal Fanconi syndromeAbdominal painAnorexiaArthralgiaIncreased circulating IgG concentrationMyalgiaAminoaciduriaElevated erythrocyte sedimentation rateHyperchloremic metabolic acidosisVitreous hemorrhageOcular hypertensionRenal tubular epithelial necrosisIncreased circulating immunoglobulin concentrationElevated circulating C-reactive protein concentrationPosterior synechiae of the anterior chamberCystoid macular edemaChoroidal neovascularizationPanuveitisIntermediate uveitisRetinal vasculitisFlank painAnterior chamber flareReduced hematocritMacular edemaScleritisAbnormal retinal pigmentationChorioretinal scarIris nevus

Classification & Codes

MeSH Code

C536922

Orphanet Code

ORPHA:91500
Tubulointerstitial nephritis and uveitis
MeSHC536922
OrphanetORPHA:91500
Treatments0 drug(s)
Symptoms on record53 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Tubulointerstitial nephritis and uveitis | OrphanDrug