typical hemolytic-uremic syndrome
ORPHA: 90038
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with typical hemolytic-uremic syndrome, sourced from HPO and Orphanet clinical annotations.
ThrombocytopeniaAcute kidney injuryMicroangiopathic hemolytic anemiaVomitingDiarrheaAbdominal painElevated circulating creatinine concentrationDysfunctional alternative complement pathwayUnconjugated hyperbilirubinemiaAnuriaAbnormality of the nervous systemIrritabilityHypertensionSeizureExcessive daytime somnolenceReticulocytosisDehydrationIncreased total leukocyte countSchistocytosisHypokalemiaHyponatremiaHemoglobinuriaBloody diarrheaIncreased circulating lactate dehydrogenase concentrationIntestinal perforationAcute colitisComaMyocardial infarctionPancreatitisRectal prolapseIntussusceptionPeritonitisColonic stenosis
Classification & Codes
Orphanet Code
ORPHA:90038typical hemolytic-uremic syndrome
| Orphanet | ORPHA:90038 |
| Treatments | 0 drug(s) |
| Symptoms on record | 33 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO