tyrosinemia type I

ICD-10: E70.2ORPHA: 69723

Overview

tyrosinemia that has material basis in deficiency of the enzyme fumarylacetoacetate hydrolase resulting in an increase in fumarylacetoacetate which inhibits previous steps in tyrosine degradation leading to an accumulation of tyrosine in the body

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

E70.2

Orphanet Code

ORPHA:69723
tyrosinemia type I
ICD-10E70.2
OrphanetORPHA:69723
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
tyrosinemia type I | OrphanDrug