ulnar-mammary syndrome

MeSH: C536937ORPHA: 3138

Overview

skin condition characterized by underdevelopment of the apocrine and mammary glands which can cause various nipple, breast and genital abnormalities, and abnormal development of fingers and forearms

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with ulnar-mammary syndrome, sourced from HPO and Orphanet clinical annotations.

Abnormal morphology of the radiusAbsent handHernia of the abdominal wallEctopic anusAbnormal metacarpal morphologyAplasia of the pectoralis major muscleShort distal phalanx of fingerArrhythmiaCamptodactyly of fingerBreast aplasiaAbnormal finger morphologyAbnormal fingernail morphologyAbsent axillary hairAbnormality of temperature regulationAplasia/Hypoplasia of the ulnaCryptorchidismAbnormality of the uterusDecreased fertilityDelayed pubertyObesityHypoplastic nipplesAbnormality of the wristShort statureHypoplasia of penisRenal hypoplasiaHypodontiaPectus carinatumAbnormal clavicle morphologySprengel anomalyPostaxial hand polydactylyLaryngomalaciaVentricular septal defectHypoplastic toenailsPyloric stenosisAnal atresiaAbnormal humerus morphology

Classification & Codes

MeSH Code

C536937

Orphanet Code

ORPHA:3138
ulnar-mammary syndrome
MeSHC536937
OrphanetORPHA:3138
Treatments0 drug(s)
Symptoms on record36 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO