Urticarial vasculitis

ICD-10: L95.8ORPHA: 36412

Overview

skin condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Urticarial vasculitis, sourced from HPO and Orphanet clinical annotations.

Renal insufficiencyProteinuriaSensorineural hearing impairmentConjunctivitisUveitisSensory neuropathyHematuriaSkin rashPruritusSeizureAtaxiaMeningitisReduced tendon reflexesArthritisJoint dislocationAscitesAbnormal heart valve morphologyPericardial effusionSplenomegalyDiarrheaNausea and vomitingAbdominal painRestrictive ventilatory defectDyspneaEmphysemaHemoptysisPleural effusionHepatomegalyLymphomaLymphadenopathyRecurrent bacterial infectionsAutoimmunityMyalgiaHemiplegia/hemiparesisReduced circulating complement concentrationAirway obstructionCranial nerve paralysisIrregular hyperpigmentationPeripheral neuropathySmall vessel vasculitisCoughCerebral palsyImmunologic hypersensitivityInflammatory abnormality of the eyeEpiscleritisAngioedemaGlomerulopathyInflammation

Classification & Codes

ICD-10 Code

L95.8

Orphanet Code

ORPHA:36412
Urticarial vasculitis
ICD-10L95.8
OrphanetORPHA:36412
Treatments0 drug(s)
Symptoms on record48 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO