Van den Ende-Gupta syndrome

MeSH: C535909ORPHA: 2460

Overview

Van den Ende-Gupta syndrome is a very rare syndrome characterized by blepharophimosis, arachnodactyly, joint contractures, and characteristic dysmorphic features

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Van den Ende-Gupta syndrome, sourced from HPO and Orphanet clinical annotations.

Long footDislocated radial head2-3 toe syndactylyDepressed nasal bridgeSlender metacarpalsBowing of the long bonesElbow contractureJoint contractureHydronephrosisNarrow mouthMicrognathiaHearing impairmentUnderdeveloped nasal alaeSclerocorneaDental crowdingDelayed speech and language developmentCraniosynostosisTalipes equinovarusDeviated nasal septumGlenoid fossa hypoplasiaAbnormal aryepiglottic fold morphologyAbnormal columella morphologyClinodactylyKnee contractureEverted lower lip vermilionMalar flatteningBlepharophimosisArachnodactylyCamptodactylyHigh palateFacial asymmetryTriangular faceProtruding earNarrow noseDownslanted palpebral fissuresThin ribsLateral clavicle hookHallux valgus

Classification & Codes

MeSH Code

C535909

Orphanet Code

ORPHA:2460
Van den Ende-Gupta syndrome
MeSHC535909
OrphanetORPHA:2460
Treatments0 drug(s)
Symptoms on record38 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO