von Economo's disease
ORPHA: 83600
Overview
atypical form of encephalitis
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with von Economo's disease, sourced from HPO and Orphanet clinical annotations.
EncephalopathySleep disturbanceDiplopiaLethargyMental deteriorationParkinsonismTremorFeverHeadacheIncreased CSF protein concentrationAutoimmunityMyalgiaUpper limb muscle weaknessRecurrent viral infectionsLimitation of neck motionBilateral basal ganglia lesionsIncreased circulating immunoglobulin concentrationAbnormal involuntary eye movementsPharyngitisDyskinesiaUrinary incontinencePhotophobiaPsychosisSeizureComaBradycardiaBowel incontinenceHyperventilationLimb painStiff neck
Classification & Codes
Orphanet Code
ORPHA:83600von Economo's disease
| Orphanet | ORPHA:83600 |
| Treatments | 0 drug(s) |
| Symptoms on record | 30 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO