Waldmann disease
ICD-10: I89.0MeSH: C536567ORPHA: 90362
Overview
medical condition
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Waldmann disease, sourced from HPO and Orphanet clinical annotations.
EdemaAnemiaIntestinal lymphangiectasiaCombined immunodeficiencyFunctional abnormality of the gastrointestinal tractAbnormal lymphatic vessel morphologyGrowth delayWeight lossDecreased total lymphocyte countChronic diarrheaHypoalbuminemiaHypoproteinemiaDecreased circulating immunoglobulin concentrationAbnormal small intestinal villus morphologyAbnormality of vitamin metabolismTetanyAscitesPericardial effusionAbdominal painPleural effusionDecreased circulating IgA concentrationDecreased circulating total IgMHypocalcemiaHypomagnesemiaMuscle spasmDecreased circulating IgG concentrationGeneralized edemaDecreased CD4+ effector memory T cell proportionIncreased stool alpha1-antitrypsin concentrationOpportunistic infectionDecreased total T cell countDecreased circulating vitamin D concentrationCryptococcal meningitisDisseminated cutaneous warts
Classification & Codes
ICD-10 Code
I89.0MeSH Code
C536567Orphanet Code
ORPHA:90362Waldmann disease
| ICD-10 | I89.0 |
| MeSH | C536567 |
| Orphanet | ORPHA:90362 |
| Treatments | 0 drug(s) |
| Symptoms on record | 34 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO