West syndrome

ICD-10: G40.4ORPHA: 505652

Overview

severe epilepsy syndrome with infantile spasms, hypsarrhythmia and mental retardation

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with West syndrome, sourced from HPO and Orphanet clinical annotations.

Generalized tonic seizureEverted lower lip vermilionBroad foreheadDeeply set eyeAutistic behaviorDelayed speech and language developmentReduced eye contactIntellectual disabilityHypotoniaGait disturbanceGrowth delayDeep philtrumConstipationGastroesophageal refluxBilateral tonic-clonic seizureDelayed gross motor developmentPoor head controlHypsarrhythmiaBruxismAbnormal muscle toneSleep-wake cycle disturbanceImpaired pain sensationFocal-onset seizureBroad proximal phalanges of the handMultifocal epileptiform dischargesProminent foreheadModerate global developmental delaySevere global developmental delayGastrostomy tube feeding in infancyFeeding difficultiesStereotypical hand wringingInfantile spasmsThick vermilion borderMyoclonic seizureColdnessCerebral visual impairmentTactile hypersensitivityMicrocephalyNarrow foreheadHigh foreheadEsotropiaExotropiaSynophrysParoxysmal bursts of laughterDystoniaHallux valgusChoreaApneaScoliosisRecurrent lower respiratory tract infectionsKyphosisHyperventilation

Classification & Codes

ICD-10 Code

G40.4

Orphanet Code

ORPHA:505652
West syndrome
ICD-10G40.4
OrphanetORPHA:505652
Treatments0 drug(s)
Symptoms on record52 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO