Whipple disease

ICD-10: K90.890.8MeSH: D008061ORPHA: 3452

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Whipple disease, sourced from HPO and Orphanet clinical annotations.

HydrocephalusProptosisUveitisDepressionHypothyroidismInsulin resistanceSeizureAtaxiaMuscle weaknessMyoclonusArthritisMyocardial infarctionPericarditisSplenomegalyAnemiaFeverPolydipsiaDiarrheaMalabsorptionAbdominal painAnorexiaRespiratory insufficiencyPleuritisGastrointestinal hemorrhageHepatomegalySleep disturbanceDevelopmental regressionInfectious encephalitisIncreased intracranial pressureHypotensionArthralgiaHyponatremiaMyalgiaCachexiaCranial nerve paralysisAbnormal pyramidal signGeneralized hyperpigmentationPeripheral neuropathyPedal edemaFatigueCoughMyocarditisMyositisErectile dysfunctionMediastinal lymphadenopathyChest painGalactorrhea

Classification & Codes

ICD-10 Code

K90.890.8

MeSH Code

D008061

Orphanet Code

ORPHA:3452
Whipple disease
ICD-10K90.890.8
MeSHD008061
OrphanetORPHA:3452
Treatments0 drug(s)
Symptoms on record47 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO