wild-type transthyretin amyloid

ORPHA: 3300011 Treatment Available

Overview

human disease

Available Treatments (1)

DrugFormStatusCountriesLead Time
Patisiran
Orphan Cold Chain
IV infusion, 2 mg/mLFDA Approved6

Clinical Presentation

Signs and symptoms associated with wild-type transthyretin amyloid, sourced from HPO and Orphanet clinical annotations.

Congestive heart failureHypertrophic cardiomyopathyMyocardial infarctionPleural effusionAbnormal EKGAbnormal pulmonary interstitial morphologyPedal edemaCardiac transthyretin amyloid depositionPulmonary edemaSensory neuropathyChronic diarrheaHepatomegalyIntermittent diarrheaImpaired vibratory sensationGastrointestinal dysmotilityBowel incontinenceElevated circulating alkaline phosphatase concentrationOrthostatic hypotension due to autonomic dysfunctionAtrial fibrillationAutonomic bladder dysfunctionArrhythmiaConstrictive median neuropathyAbnormal autonomic nervous system physiologyDecreased/absent ankle reflexesRenal insufficiencyProteinuriaNephrotic syndromeNephropathyAortic valve stenosisBradycardiaWeight lossSpinal canal stenosis

Classification & Codes

Orphanet Code

ORPHA:330001
wild-type transthyretin amyloid
OrphanetORPHA:330001
Treatments1 drug(s)
Symptoms on record32 signs
Statuspublished

Treatment Summary

Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO