wormian bone-multiple fractures-dentinogenesis imperfecta-skeletal dysplasia

MeSH: C565734ORPHA: 166277

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with wormian bone-multiple fractures-dentinogenesis imperfecta-skeletal dysplasia, sourced from HPO and Orphanet clinical annotations.

DolichocephalyHypertelorismPeriorbital fullnessDentinogenesis imperfectaLimitation of joint mobilityShort footToe clinodactylyWormian bonesPathologic fractureAbnormal cortical bone morphologyShort statureUpper limb undergrowthConcave nasal ridge

Classification & Codes

MeSH Code

C565734

Orphanet Code

ORPHA:166277
wormian bone-multiple fractures-dentinogenesis imperfecta-skeletal dysplasia
MeSHC565734
OrphanetORPHA:166277
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO