X-linked intellectual disability-cardiomegaly-congestive heart failure syndrome

ORPHA: 324410

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with X-linked intellectual disability-cardiomegaly-congestive heart failure syndrome, sourced from HPO and Orphanet clinical annotations.

Overfolded helixMacrotiaAbnormal thumb morphologySeizureGlobal developmental delayAbsent speechCongestive heart failureCardiomegalyProfound intellectual disabilityContractures of the large jointsAbnormal atrioventricular valve morphologyMacroorchidismEverted lower lip vermilionCoarse facial featuresMandibular prognathiaSmooth philtrumBulbous noseProminent nasal bridgeMitral valve prolapseAortic valve stenosisMitral regurgitationPoor speechSpastic tetraplegiaInability to walkKyphoscoliosisSteppage gaitAtrial flutterTricuspid regurgitationDepressed nasal bridgeProtruding tongue

Classification & Codes

Orphanet Code

ORPHA:324410
X-linked intellectual disability-cardiomegaly-congestive heart failure syndrome
OrphanetORPHA:324410
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO