X-linked intellectual disability-psychosis-macroorchidism syndrome

ORPHA: 3077

Overview

syndromic X-linked intellectual disability characterized by moderate intellectual deficit, manic-depressive psychosis, pyramidal signs and macroorchidism that has material basis in mutation in the MECP2 gene on chromosome Xq28

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with X-linked intellectual disability-psychosis-macroorchidism syndrome, sourced from HPO and Orphanet clinical annotations.

Hyperactive deep tendon reflexesTremorCongestive heart failureAnorexiaLower limb spasticityModerate intellectual disabilityLower limb hyperreflexiaShort statureBipolar affective disorderSevere intellectual disabilityFocal EEG discharges with secondary generalizationStrokeParkinsonismObesityBroad-based gaitResting tremorShuffling gaitKyphoscoliosisStooped postureAbnormal fear-induced behaviorMacroorchidismAggressive behaviorIrritabilityHyperactivitySeizureSleep disturbance

Classification & Codes

Orphanet Code

ORPHA:3077
X-linked intellectual disability-psychosis-macroorchidism syndrome
OrphanetORPHA:3077
Treatments0 drug(s)
Symptoms on record26 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO