xanthinuria

MeSH: C562584ORPHA: 3467

Overview

purine-pyrimidine metabolic disorder characterized by deficiency of xanthine oxidase, resulting in excretion of large amounts of xanthine in the urine and the formation of xanthine stones

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with xanthinuria, sourced from HPO and Orphanet clinical annotations.

HypouricemiaDecreased urinary urateUric acid nephrolithiasisXanthine nephrolithiasisAldehyde oxidase deficiencyReduced xanthine dehydrogenase levelSulfite oxidase deficiencyHyperxanthinemiaXanthinuriaIncreased urinary hypoxanthine levelCrystalluriaRecurrent urinary tract infectionsHematuriaAcute kidney injuryArthropathyMyopathyMyalgiaMuscle spasmChronic kidney diseaseFlank painGout

Classification & Codes

MeSH Code

C562584

Orphanet Code

ORPHA:3467
xanthinuria
MeSHC562584
OrphanetORPHA:3467
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO