Yemenite deaf-blind hypopigmentation syndrome

MeSH: C536771ORPHA: 3214

Overview

The Yemenite deaf-blind hypopigmentation syndrome, also called Warburg-Thomsen syndrome, is an extremely rare genetic disorder characterized by skin pigmentation abnormalities, eye disorders, and hearing loss.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Yemenite deaf-blind hypopigmentation syndrome, sourced from HPO and Orphanet clinical annotations.

Sensorineural hearing impairmentStrabismusNystagmusDelayed eruption of teethHyperpigmentation of the skinHypopigmented skin patchesFrecklingMacrodontiaHypopigmentation of hairMultiple cafe-au-lait spotsShort philtrumHigh foreheadMicrocorneaIris colobomaGait disturbanceIris hypopigmentationAnterior synechiae of the anterior chamberTaurodontiaHypertoniaHigh, narrow palateHigh hypermetropiaAbnormal size of the palpebral fissures

Classification & Codes

MeSH Code

C536771

Orphanet Code

ORPHA:3214
Yemenite deaf-blind hypopigmentation syndrome
MeSHC536771
OrphanetORPHA:3214
Treatments0 drug(s)
Symptoms on record22 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO