Zollinger–Ellison syndrome

MeSH: D015043ORPHA: 913

Overview

disease of the digestive tract in which tumors lead to excess acid and peptic ulcers

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Zollinger–Ellison syndrome, sourced from HPO and Orphanet clinical annotations.

Zollinger-Ellison syndromeNeuroendocrine neoplasmDiarrheaNauseaEpisodic abdominal painDuodenal ulcerPeptic ulcerEsophagitisWeight lossHyperparathyroidismElevated circulating growth hormone concentrationThyroid adenomaJaundiceMultiple lipomasGastrointestinal hemorrhageHematocheziaPituitary adenomaHypercalcemiaIncreased circulating cortisol levelElevated circulating parathyroid hormone levelIntestinal obstructionPituitary prolactin cell adenomaParathyroid hyperplasiaAdrenocortical adenomaPituitary corticotropic cell adenomaErythemaPituitary growth hormone cell adenomaPituitary null cell adenomaIncreased urinary cortisol levelLipomaExtrahepatic cholestasisGlucagonomaIncreased glucagon levelAdrenocortical carcinoma

Classification & Codes

MeSH Code

D015043

Orphanet Code

ORPHA:913
Zollinger–Ellison syndrome
MeSHD015043
OrphanetORPHA:913
Treatments0 drug(s)
Symptoms on record34 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO