mitapivat

Orphan DrugFDA Approved (2022), EMA Approved (2022)

Description

Mitapivat is a first-in-class oral pyruvate kinase (PK) activator for hemolytic anemia due to pyruvate kinase deficiency (PKD). It enhances the activity of deficient PK enzymes, improving red blood cell survival and reducing hemolysis. This represents a significant advance for a disease previously managed only with transfusions and splenectomy.

Indications & Therapeutic Use

Hemolytic anemia due to pyruvate kinase (PK) deficiency in adults

Linked Diseases:

Global Availability (5 countries)

CountryAccess RouteRegulatory PathwayLead TimeStatus

Available Through

This drug is available for procurement through the following fulfilment partner.

Fulfilment Partner
mitapivat
Generic Namemitapivat
Brands1 brand available
Active Ingredientmitapivat sulfate
Drug ClassHemolytic anemia due to pyruvate kinase (PK) deficiency in adults
ManufacturerAgios Pharmaceuticals
Dosage FormsOral tablet, 5mg, 20mg, 50mg
Medical CodeB06AX02
Orphan StatusYes — Orphan Drug
Cold ChainNot Required
Lead Time10 days
Reg. StatusFDA Approved (2022), EMA Approved (2022)
Clinical TrialNCT03853798
Countries5 countries
Authority Signals
Last Verified3/21/2026
Data ConfidenceHigh (AI + Pharmacist)
Source Citations6 Validated Nodes