hypertrophic cardiomyopathy 13

MeSH: C567686ORPHA: 1552 Treatments Available

Overview

hypertrophic cardiomyopathy that has material basis in heterozygous mutation in the TNNC1 gene on chromosome 3p21

Available Treatments (2)

DrugFormStatusCountriesLead Time
mavacamten
Orphan
oral capsule, 2.5mg, 5mg, 10mg, 15mgFDA Approved914d
disopyramide
oral capsule, 100mg, 150mg; extended-release capsule, 100mg, 150mgFDA Approved77d

Classification & Codes

MeSH Code

C567686

Orphanet Code

ORPHA:155
hypertrophic cardiomyopathy 13
MeSHC567686
OrphanetORPHA:155
Treatments2 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO