carglumic acid

Orphan DrugFDA Approved, EMA Approved

Description

Carglumic acid is a synthetic structural analogue of N-acetylglutamate (NAG), which serves as an essential cofactor for the first enzyme in the urea cycle. It is used as adjunctive therapy for the treatment of acute hyperammonemia and maintenance therapy for chronic hyperammonemia due to N-acetylglutamate synthase (NAGS) deficiency. The drug can also be used in certain organic acidemias including methylmalonic acidemia.

Indications & Therapeutic Use

hyperammonemia due to N-acetylglutamate synthase deficiency, acute hyperammonemia in organic acidemias including methylmalonic acidemia

Global Availability (8 countries)

CountryAccess RouteRegulatory PathwayLead TimeStatus

Available Through

This drug is available for procurement through the following fulfilment partner.

Fulfilment Partner
carglumic acid
Generic Namecarglumic acid
Brands1 brand available
Active Ingredientcarglumic acid
Drug Classhyperammonemia due to N-acetylglutamate synthase deficiency
ManufacturerRecordati Rare Diseases
Dosage FormsOral dispersible tablets, 200mg
Medical CodeA16AA05
Orphan StatusYes — Orphan Drug
Cold ChainNot Required
Lead Time14 days
Reg. StatusFDA Approved, EMA Approved
Clinical TrialNCT00551200
Countries8 countries
Authority Signals
Last Verified3/21/2026
Data ConfidenceHigh (AI + Pharmacist)
Source Citations9 Validated Nodes