Lomitapide

Orphan DrugFDA Approved

Description

Lomitapide is a microsomal triglyceride transfer protein (MTP) inhibitor indicated as an adjunct to a low-fat diet and other lipid-lowering treatments, including apheresis, to reduce low-density lipoprotein cholesterol (LDL-C), total cholesterol (TC), apolipoprotein B (apo B), and non-high-density lipoprotein cholesterol (non-HDL-C) in patients with homozygous familial hypercholesterolemia (HoFH). It is used to treat familial dysbetalipoproteinemia.

Indications & Therapeutic Use

Homozygous Familial Hypercholesterolemia, Familial Dysbetalipoproteinemia

Linked Diseases:

Global Availability (4 countries)

CountryAccess RouteRegulatory PathwayLead TimeStatus

Available Through

This drug is available for procurement through the following fulfilment partner.

Fulfilment Partner
Lomitapide
Generic NameLomitapide
Brands1 brand available
Active IngredientLomitapide
Drug ClassHomozygous Familial Hypercholesterolemia
ManufacturerAegerion Pharmaceuticals
Dosage FormsCapsule
Medical CodeC10AX12
Orphan StatusYes — Orphan Drug
Cold ChainNot Required
Reg. StatusFDA Approved
Countries4 countries
Authority Signals
Last Verified3/21/2026
Data ConfidenceHigh (AI + Pharmacist)
Source Citations5 Validated Nodes